List of NEW ICD-10 CM codes for 2026 Chaptewise for coders

Chapter 1 – Infectious/Parasitic Diseases

B88.01 – Infestation by Demodex mites
– AKA “face mites”
B88.09 – Other acariasis

 

Chapter 2 – Neoplasms

C50.A0 – Malignant inflammatory neoplasm of unspecified, breast
C50.A1 – Malignant inflammatory neoplasm of right breast
C50.A2 – Malignant inflammatory neoplasm of left breast

 

Chapter 3 – Blood/Blood Forming Organs

Includes new codes for:

  • Leukocyte adhesion deficiency
  • Other functional disorders of polymorphonuclear neutrophils
  • Functional disorders of polymorphonuclear neutrophils, unspecified

• D71.1 – Leukocyte adhesion deficiency
• D71.8 – Other functional disorders of polymorphonuclear neutrophils
• D71.9 – Functional disorders of polymorphonuclear neutrophils, unspecified

 

Chapter 4 – Endocrine/Metabolic

Includes new codes for:

  • Type 2 diabetes mellitus without complications in remission
  • Primary and secondary hyperoxaluria
  • Familial hypercholesterolemia
  • Other disorders of mineral metabolism
  • Lipodystrophy, not elsewhere classified
  • Mitochondrial metabolism disorders

E11.A – Type 2 diabetes mellitus without complications in remission

E72.530 – Primary hyperoxaluria, type 1
E72.538 – Other primary hyperoxaluria
 E72.539 – Primary hyperoxaluria, unspecified
 E72.540 – Dietary hyperoxaluria
 E72.541 – Enteric hyperoxaluria
 E72.548 – Other secondary hyperoxaluria
 E72.549 – Secondary hyperoxaluria, unspecified

E78.010 – Homozygous familial hypercholesterolemia [HoFH]
 E78.011 – Heterozygous familial hypercholesterolemia [HeFH]}
 E78.019 – Familial hypercholesterolemia, unspecified

E83.820 – Generalized arterial calcification of infancy with unspecified genetic causality
 E83.821 – ENPP1 deficiency causing generalized arterial calcification of infancy
 E83.822 – ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
 E83.823 – ABCC6 deficiency causing generalized arterial calcification of infancy
 E83.824 – ABCC6 deficiency causing pseudoxanthoma elasticum • E83.825 – CD73 deficiency causing arterial calcification

E88.10 – Lipodystrophy, unspecified
 E88.11 – Partial lipodystrophy
 E88.12 – Generalized lipodystrophy
 E88.13 – Localized lipodystrophy
 E88.14 – HIV-associated lipodystrophy
 E88.19 – Other lipodystrophy, NEC

Chapter 6 – Nervous

Includes new codes for:

  • Primary progressive apraxia of speech
  • Relapsing-remitting multiple sclerosis
  • Primary and secondary progressive multiple sclerosis
  • Multiple sclerosis, unspecified
  • Limb girdle muscular dystrophies

G31.87 – Primary progressive apraxia of speech
 G71.036 – Limb girdle muscular dystrophy due to fukutin related protein dysfunction

G35.A – Relapsing -remitting multiple sclerosis
 G35.B0 – Primary progressing multiple sclerosis, unspecified
 G35.B1 – Active primary progressive multiple sclerosis
 G35.C0 – Secondary progressive multiple sclerosis, unspecified
 G35.C1 – Active secondary progressive multiple sclerosis
 G35.C2 – Non -active secondary progressive multiple sclerosis
 G35.D – Multiple sclerosis, unspecified

Chapter 7 – Eye

Category H01.8- Other specified inflammation (right/left and upper/lower
eyelids)
 H05.831 – Thyroid orbitopathy, right orbit
 H05.832 – Thyroid orbitopathy, left orbit
 H05.833 – Thyroid orbitopathy, bilateral
 H05.839 – Thyroid orbitopathy, unspecified orbit

H40.841 – Neovascular secondary angle closure glaucoma, right eye
 H40.842 – Neovascular secondary angle closure glaucoma, left eye
 H40.843 – Neovascular secondary angle closure glaucoma, bilateral
 H40.849 – Neovascular secondary angle closure glaucoma, unspecified eye

Chapter 9 – Circulatory

I27.840 – Fontan-associated liver disease [FALD]
 I27.841 – Fontan-associated lymphatic dysfunction
 I27.848 – Other Fontan-associated condition
 I27.849 – Fontan-related circulation, unspecified

Chapter 12 – Skin/Subcutaneous Tissues

Includes new codes for:

  • Cutaneous abscess of flank
  • Furuncle of flank
  • Cellulitis of flank
  • Acute lymphangitis of flank
  • Non-pressure chronic ulcer abdomen, chest, neck, face, and groin
  • Non-pressure chronic ulcer of upper limb, not elsewhere classified
  • Non-pressure chronic ulcer of upper arm
  • Non-pressure chronic ulcer of forearm
  • Non-pressure chronic ulcer of hand
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L02.217 – Cutaneous abscess of flank
 L02.227 – Furuncle of flank
 L03.31A – Cellulitis of flank
 L03.32A – Acute lymphangitis of flank

Chapter 13 – Musculoskeletal

M05.A – Abnormal rheumatoid factor and anti-citrullinated protein antibody with
rheumatoid arthritis

Chapter 14 – Genitourinary

Includes new codes for:

  • Acute nephritic syndrome with immune complex membranoproliferative glomerulonephritis
  • Nephrotic syndrome with immune complex membranoproliferative glomerulonephritis
  • Hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease

N00.B1 –Acute nephritic syndrome with idiopathic immune membranoproliferative glomerulonephritis (IC-MPGN)
 N00.B2 – Acute nephritic syndrome with secondary immune complex membranoproliferative glomerulonephritis
 N04.B1 – Nephrotic syndrome with idiopathic immune membranoproliferative glomerulonephritis
N04.B2 – Nephrotic syndrome with secondary immune complex membranoproliferative glomerulonephritis
 N07.B – Hereditary nephropathy, NEC with APOL-1-mediated kidney disease

Chapter 17 – Congenital

Includes new codes for:

  • Hao-Fountain Syndrome
  • CTNNB1 syndrome
  • Kabuki syndrome
  • other specified congenital malformations
  • Usher syndrome
  • Other specified chromosome abnormalities
  • Genetic disorders, not elsewhere classified
  • Neurodevelopmental disorders related to specific genetic pathogenic variants
  • Neurodevelopmental disorders related to pathogenic variants in specific genes
  • Neurodevelopmental disorders related to pathogenic variants in other specific genes

Q87.87 – Hao-Fountain syndrome
 Q87.88 – CTNNB1 syndrome
 Q89.81 – Kabuki syndrome

Q89.89 – Other specified congenital malformations
 Q99.89 – Other specified chromosome abnormalities

Q99.811 – Usher syndrome, Type 1
 Q99.812 – Usher syndrome, Type 2
 Q99.813 – Usher syndrome, Type 3
 Q99.818 – Other Usher syndrome
 Q99.819 – Usher syndrome, unspecified

QA0.0101 – SCN2A-related neurodevelopmental disorder
 QA0.0102 – CACNA1A-related neurodevelopmental disorder
 QA0.0109 – Neurodevelopmental disorder related to  pathogenic variant in other ion channel gene
 QA0.011 – Neurodevelopmental disorders related to pathogenic variants in glutamate receptor genes
 QA0.0131 – SLC6A1-releated disorder

QA0.0131 – SLC6A1-releated disorder
 QA0.0139 – Neurodevelopmental disorder related to pathogenic variant in other transporter or solute carrier gene
 QA0.0141 – Syntaxin-binding protein 1-related disorder 
 QA0.0142 – DLG4-related synaptopathy
 QA0.0149 – Neurodevelopmental disorder, related to pathogenic variant in other synapse related gene

QA0.0151 – FOXG syndrome
 QA0.0159 – Neurodevelopmental disorder, related to other genes associated with transcription and gene expression 
 QA0.8 – Other neurodevelopmental disorders related to pathogenic variants in other specific genes

Chapter 18 – Symptoms/Signs

Includes new codes for:

  • Pelvic and perineal pain
  • Abdominal pain of multiple sites
  • Flank tenderness
  • Pain localized to flank
  • Cannabis hyperemesis syndrome
  • Costovertebral (angle) tenderness
  • Abnormal rheumatoid factor and anti-citrullinated protein antibody without rheumatoid arthritis
  • Other specified abnormal immunological findings in serum

R10.20 – Pelvic and perineal pain, unspecified side
 R10.21 – Pelvic and perineal pain, right side
 R10.22 – Pelvic and perineal pain, left side
 R10.23 – Pelvic and perineal pain, bilateral
 R10.24 – Suprapubic pain

R10.85 – Abdominal pain of multiple sites
 R10.8A1 – Right flank tenderness
 R10.8A2 – Left flank tenderness
 R10.8A3 – Suprapubic tenderness
 R10.8A9 – Flank tenderness, unspecified
 R10.A0 – Flank pain, unspecified side
 R10.A1 – Flank pain, right side
 R10.A2 – Flank pain, left side
 R10.A3 – Flank pain, bilateral

R11.16 – Cannabis hyperemesis syndrome

R39.851 – Costovertebral (angle) tenderness, right side
 R39.852 – Costovertebral (angle) tenderness, left side
 R39.853 – Costovertebral (angle) tenderness, bilateral
 R39.859 – Costovertebral (angle) tenderness, unspecified side

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R76.81 – Abnormal rheumatoid factor and anti-citrullinated protein antibody
without rheumatoid arthritis

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R76.89 – Other specified abnormal immunological findings in serum

Chapter 19 – Injury/Poisonings

Includes new codes for:

  • Contusion of abdominal wall
  • Contusion of groin
  • Contusion of flank (latus) region
  • Abrasion of flank
  • Blister (nonthermal) of flank
  • External constriction of flank
  • Superficial foreign body of flank
  • Insect bite (nonvenomous) of flank
  • Other superficial bite of flank
  • Unspecified superficial injury of flank
  • Unspecified open wound of abdominal wall without penetration into peritoneal cavity
  • Laceration without foreign body of abdominal wall without penetration into peritoneal cavity
  • Laceration without foreign body of abdominal wall without penetration into peritoneal cavity
  • Puncture wound of abdominal wall without foreign body without penetration into peritoneal cavity
  • Puncture wound of abdominal wall with foreign body without penetration into peritoneal cavity
  • Open bite of abdominal wall without penetration into peritoneal cavity
  • Unspecified open wound of abdominal wall with penetration into peritoneal cavity
  • Laceration without foreign body of abdominal wall with penetration into peritoneal cavity
  • Laceration with foreign body of abdominal wall with penetration into peritoneal cavity
  • Puncture wound without foreign body of abdominal wall with penetration into peritoneal cavity
  • Puncture wound with foreign body of abdominal wall with penetration into peritoneal cavity
  • Open bite of abdominal wall with penetration into peritoneal cavity
  • Poisoning by, adverse effect of and underdosing of fluoroquinolone antibiotics
  • Toxic effect of xylazine
  • Effects of war theater
  • Anaphylactic reaction due to milk and dairy products
  • Anaphylactic reaction due to eggs
  • Other adverse food reactions due to milk and dairy products
  • Other adverse food reaction due to eggs
  • Other adverse food reactions, not elsewhere classified

S30-S31 for injuries involving abdominal wall, groin and flank

– Contusions
– Abrasions
– Blisters
– Superficial foreign body
– Insect bites
– Open wounds
– Lacerations
– Puncture wounds
– Open bite

T36.AX1- Poisoning, adverse effect of, underdosing of fluoroquinolone

 Requires 7th character for episode of care

T75.830- Gulf war illness
 Requires 7th character for episode of care

T75.838- Effects of other war theater
Requires 7th character for episode of care

T78.070– Anaphylactic reaction due to milk/dairy products with tolerance to baked milk
 T78.071- Anaphylactic reaction due to milk/dairy products with reactivity to baked milk
 T78.079- Anaphylactic reaction due to milk/dairy products, unspecified 
 Requires 7th character for episode of care

T78.080– Anaphylactic reaction due to egg with tolerance to baked egg
 T78.081- Anaphylactic reaction due to egg with reactivity to baked egg
 T78.089- Anaphylactic reaction due to eggs, unspecified
 Requires 7th character for episode of care

T78.110– Other adverse food reactions due to milk/dairy products with tolerance to baked milk
 T78.111- Other adverse food reactions due to milk/dairy products with reactivity to baked milk
 T78.119– Other adverse food reactions due to milk/dairy products with baked milk tolerance/reactivity, unspecified
 Requires 7th character for episode of care

T78.120 – Other adverse food reaction due to egg with tolerance to baked egg
 T78.121 – Other adverse food reaction due to egg with reactivity to baked egg
 T78.129 – Other adverse food reaction due to egg, with baked egg tolerance/reactivity unspecified
 T78.19X- Other adverse food reactions, NEC
 Requires 7th character for episode of care

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Chapter 20 – External Causes

Includes new codes for:

  • Other sharp object entering into or through a natural orifice
  • Fishing hook entering through skin
  • Blast overpressure in war operations
  • Blast overpressure in military operations
  • Other outdoor activity

W44.H9X- Other sharp object entering into or through a natural orifice
 W45.3XX- Fish hook entering through skin
 Requires 7th character for episode of care

 Y36.A1X- Low level blast overpressure in war operations
 Y36.A2X – High level blast overpressure in war operations
 Y37.A1X- Low level blast overpressure in military operations
 Y37.A2X – High level blast overpressure in military operations
 Requires 7th character for episode of care

Y93.L1- Activity, splitting wood
 Y93.L9 – Activity, other outdoor activity

Chapter 21 – Factors Influencing Health

Includes new codes for:

  • Genetic susceptibility to malignant neoplasm
  • Genetic susceptibility to kidney disease
  • Encounter for other prophylactic surgery
  • Financial insecurity
  • Contact with and (suspected) exposure to war theater
  • Family history of malignant neoplasm of fallopian tube(s)
  • Family history of disorders of kidney and ureter
  • Family history of exposure to diethylstilbestrol
  • Personal history of malignant neoplasm of fallopian tube(s)
  • Personal history of in-situ neoplasm of the fallopian tube(s)
  • Allergy to milk products
  • Allergy to eggs
  • Personal risk factor of exposure to diethylstilbestrol

 Z15.05 – Genetic susceptibility to malignant neoplasm of fallopian tube(s)
 Z15.060 – Genetic susceptibility to colorectal cancer
 Z15.068 – Genetic susceptibility to other malignant neoplasm of digestive
system
 Z15.07 – Genetic susceptibility to malignant neoplasm of urinary tract
 Z15.3 – Genetic susceptibility to kidney disease

Z40.81 – Encounter for prophylactic surgery for removal of ovary(s) for persons without known genetic/familial risk factors
 Z40.82 – Encounter for prophylactic surgery for removal of fallopian tube(s) for persons without known genetic/familial risk factors
 Z40.89 – Encounter for other prophylactic surgery

 Z59.861 – Financial insecurity, difficulty paying for utilities
 Z59.868– Other specific financial insecurity
 Z59.869 – Financial insecurity, unspecified

Z77.31 – Contact with and (suspected) exposure to Gulf War theater
 Z77.39 – Contact with and (suspected) exposure to other war theater

Z80.44 – Family history of malignant neoplasm of fallopian tube(s)
 Z84.11 – Family history of APOL-1 mediated kidney disease [AKMD]
 Z84.19 – Family history of other disorders of kidney and  ureter(s)
 Z84.A – Family history of exposure to diethylstilbestrol
 Z85.4A – Personal history of malignant neoplasm of fallopian tube(s)
 Z86.00A – Personal history of in-situ neoplasm of the fallopian tubes

Z91.0110 – Allergy to milk products, unspecified
 Z91.0111 – Allergy to milk products with tolerance to baked milk
 Z91.0112 – Allergy to milk products with reactivity to baked milk
 Z91.0120 – Allergy to eggs, unspecified
 Z91.0121 – Allergy to eggs with tolerance to baked egg
 Z91.0122 – Allergy to eggs with reactivity to baked egg
 Z91.B – Personal risk factor of exposure to diethylstilbestrol

Author

  • Jitendra M.Sc CPC

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